CORDISCO HEMANGIOMA PDF

Rapidly involuting congenital haemangioma RICH may present with thrombocytopenia, low fibrinogen and elevated fibrin degradation products and D-dimers. Such complications have rarely been reported. We wished to define the clinical characteristics of the thrombocytopenia and coagulopathy associated with RICH, to emphasize the transient nature of this haematological complication and to distinguish these abnormalities from true Kasabach-Merritt phenomenon KMP. We present a case series of seven patients with large RICH who presented with thrombocytopenia and coagulopathy during the first week of life.

Author:Kasho Zulut
Country:Colombia
Language:English (Spanish)
Genre:Relationship
Published (Last):16 August 2009
Pages:313
PDF File Size:8.82 Mb
ePub File Size:14.72 Mb
ISBN:847-1-58974-518-1
Downloads:84796
Price:Free* [*Free Regsitration Required]
Uploader:JoJokinos



Rapidly involuting congenital haemangioma RICH may present with thrombocytopenia, low fibrinogen and elevated fibrin degradation products and D-dimers. Such complications have rarely been reported. We wished to define the clinical characteristics of the thrombocytopenia and coagulopathy associated with RICH, to emphasize the transient nature of this haematological complication and to distinguish these abnormalities from true Kasabach-Merritt phenomenon KMP.

We present a case series of seven patients with large RICH who presented with thrombocytopenia and coagulopathy during the first week of life. Clinical and haematological characteristics were recorded retrospectively.

Two of the patients were treated with embolization due to early signs of high-output cardiac failure; four patients received oral corticosteroids in the range of 2 mg kg -1 daily; one patient did not receive any treatment in the neonatal period, although the tumour was excised at 6 months of age. Two patients with platelet counts lower than 10 x 10 9 L -1 received a platelet transfusion.

There were no bleeding complications and only one patient presented with petechiae. However, in contrast to true KMP, these abnormal laboratory findings are self-limited and are usually not complicated by bleeding problems.

This site needs JavaScript to work properly. Please enable it to take advantage of the complete set of features! Clipboard, Search History, and several other advanced features are temporarily unavailable.

Search: Search. Advanced Clipboard. Create file Cancel. Email citation To:. Format: Summary Summary text Abstract Abstract text. Send email Cancel. Add to Collections Create a new collection Add to an existing collection. Name your collection: Name must be less than characters.

Choose a collection: Unable to load your collection due to an error Please try again. Add Cancel. Add to My Bibliography My Bibliography. Unable to load your delegates due to an error Please try again. Your saved search Name of saved search:. Search terms:. Test search terms. Would you like email updates of new search results? Email: change. Frequency: Monthly Weekly Daily. Which day? Send at most: 1 item 5 items 10 items 20 items 50 items items items.

Send even when there aren't any new results. Optional text in email:. Save Cancel. Create a file for external citation management software Create file Cancel. Full-text links Cite Favorites. Abstract Rapidly involuting congenital haemangioma RICH may present with thrombocytopenia, low fibrinogen and elevated fibrin degradation products and D-dimers.

Similar articles Successful transcutaneous arterial embolization of a giant hemangioma associated with high-output cardiac failure and Kasabach-Merritt syndrome in a neonate: a case report. Hosono S, et al. J Perinat Med. PMID: Kasabach-Merritt phenomenon. Al-Mazrou KA, et al. Saudi Med J. Kasabach-Merritt syndrome: therapeutic considerations. Larsen EC, et al. Kasabach-Merritt syndrome: a case review. Szlachetka DM. Neonatal Netw. PMID: Review. Kasabach-merritt phenomenon: case series and retrospective review of the mayo clinic experience.

Rodriguez V, et al. J Pediatr Hematol Oncol. Show more similar articles See all similar articles. Radhakrishna V, et al. J Indian Assoc Pediatr Surg. Epub Jan Kaposiform hemangioendothelioma: current knowledge and future perspectives.

Ji Y, et al. Orphanet J Rare Dis. Advances in the Medical Management of Vascular Anomalies. Ricci KW. Semin Intervent Radiol. Epub Sep Venous Thromboembolism in Pediatric Vascular Anomalies. Nakano TA, Zeinati C. Nakano TA, et al. Front Pediatr. The importance of early diagnosis and treatment of kaposiform hemangioendothelioma complicated by Kasabach-Merritt phenomenon.

Vivas-Colmenares GV, et al. Dermatol Pract Concept. Show more "Cited by" articles See all "Cited by" articles. Publication types Case Reports Actions. Female Actions. Humans Actions. Infant, Newborn Actions. Male Actions. Platelet Count Actions. Remission, Spontaneous Actions. Treatment Outcome Actions. Substances Fibrinogen Actions. Full-text links [x] Wiley.

Copy Download.

DONDE CRUZAN LOS BRUJOS TAISHA ABELAR PDF

Hemangiomas of Infancy: Epidemiology

While ulceration is a common, predominantly benign complication in infantile hemangioma, little is known about the prognosis of ulcerated CH. However, it has been observed that ulcerated CH may be complicated by life-threatening bleeding episodes. In both cases, the CHs were fed by high-flow vessels and the ensuing massive bleeding was due to superficial vessel wall erosion induced by the ulceration. Both patients were successfully treated with intravascular embolization; one patient underwent additional hemostatic surgery. Embolization is the treatment of choice in the case of severe bleeding, as the natural history of RICH is to spontaneously regress.

IDEAL CONCORD WRS PDF

Hemangiomas and Vascular Malformations

Since the first edition of this book was published, much new knowledge has been gained on hemangiomas and vascular malformations. This revised and updated second edition, written by worldwide leaders in the field, fully reflects this progress. Important improvements in the treatment of hemangiomas are reviewed, including the use of beta-blockers and other medical therapies as well as advances in interventional treatments and the treatment of hemangiomas in specific locations. Vascular malformations are being investigated with increasing frequency all over the world and new challenges are emerging regarding both diagnosis and treatment.

BEHRINGER CT100 PDF

We performed a retrospective case series of IHs with prolonged growth to further characterize these lesions and their treatment. Recognition of this subset of hemangiomas is important for clinicians, and further study of IHs may provide clues to their pathogenesis. Infantile hemangiomas are the most common tumor of infancy and have a well-described natural history of rapid growth during early infancy followed by gradual involution. Although there are other types of vascular tumors sometimes referred to under the umbrella term hemangiomas eg, lobular capillary hemangioma [pyogenic granuloma] , hereafter in this article the term hemangioma will refer to infantile hemangiomas specifically. The duration of the growth phase can be variable, but it has long been reported that most hemangiomas reach their maximal size within the first 6 to 10 months of life.

ALAIN DE BOTTON ENSAYOS DE AMOR PDF

Hemangiomas and Vascular Malformations pp Cite as. Few reports about the epidemiology of infantile hemangiomas IH exist and prospective studies are missing; it is difficult to provide some data. The incidence in the general newborn population is between 1. The majority of hemangiomas occur sporadically; however, familial occurrence of IH has been reported. Although IH can be seen in all races, they are more common in Caucasian infants, and less common in those of African or Asian descent.

Related Articles